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Chudasama B, Parmar Z, Desai S, Rajpura H, Jetly D and Nilkanthe R
The primary pulmonary artery sarcomas are rarely seen, can imitate pulmonary thromboembolism. The prognosis of patients with pulmonary artery sarcomas is dependent on its early and accurate diagnosis. Placed below is a description of a case of a 51-year-old man presented with dry cough and breathlessness was initially thought to have a Koch's lesion. AKT was given but the patient did not improve. Then on CT pulmonary angiography patient was suspected of having pulmonary embolus or hypo attenuating mass lesion and was given anticoagulation with unfractionated heparin, which was ineffective. CT guided biopsy of an enlarged right hilar nodal mass led to the diagnosis of primary pulmonary artery sarcoma.